Phage Display Selected Cyclic Peptide Inhibitors of Kallikrein-Related Peptidases 5 and 7 and Their In Vivo Delivery to the Skin by Gonschorek, Patrick, Zorzi, Alessandro, Maric, Tamara, Le Jeune, Mathilde, Schüttel, Mischa, Montagnon, Mathilde, Gómez-Ojea, Rebeca, Vollmar, Denis Patrick, Whitfield, Chantal, Reymond, Luc, Carle, Vanessa, Verma, Hitesh, Schilling, Oliver, Hovnanian, Alain, Heinis, Christian

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Pseudoxanthoma elasticum: a clinical, pathophysiological and genetic update including 11 novel ABCC6 mutations by Chassaing, N, Martin, L, Calvas, P, Le Bert, M, Hovnanian, A

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A new nonsense mutation in the POGLUT1 gene in two sisters with Dowling–Degos disease by Duchatelet, S., Clerc, H., Machet, L., Gaboriaud, P., Miskinyte, S., Kervarrec, T., Hovnanian, A.

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Successful treatment of JAK1-associated inflammatory disease by Fayand, Antoine, Hentgen, Véronique, Posseme, Céline, Lacout, Carole, Picard, Capucine, Moguelet, Philippe, Cescato, Margaux, Sbeih, Nabiha, Moreau, Thomas R.J., Zhu, Yixiang Y.J., Charuel, Jean-Luc, Corneau, Aurélien, Deibener-Kaminsky, Joelle, Dupuy, Stéphanie, Fusaro, Mathieu, Hoareau, Benedicte, Hovnanian, Alain, Langlois, Vincent, Le Corre, Laurent, Maciel, Thiago T., Miskinyte, Snaigune, Miyara, Makoto, Moulinet, Thomas, Perret, Magali, Schuhmacher, Marie Hélène, Rignault-Bricard, Rachel, Viel, Sébastien, Vinit, Angélique, Soria, Angèle, Duffy, Darragh, Launay, Jean-Marie, Callebert, Jacques, Herbeuval, Jean Philippe, Rodero, Mathieu P., Georgin-Lavialle, Sophie

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AXIN2 germline testing in a French cohort validates pathogenic variants as a rare cause of predisposition to colorectal polyposis and cancer by Leclerc, Julie, Beaumont, Marie, Vibert, Roseline, Pinson, Stéphane, Vermaut, Catherine, Flament, Cathy, Lovecchio, Tonio, Delattre, Lucie, Demay, Christophe, Coulet, Florence, Guillerm, Erell, Hamzaoui, Nadim, Benusiglio, Patrick R., Brahimi, Afane, Cornelis, François, Delhomelle, Hélène, Fert‐Ferrer, Sandra, Fournier, Benjamin P. J., Hovnanian, Alain, Legrand, Clémentine, Lortholary, Alain, Malka, David, Petit, Florence, Saurin, Jean‐Christophe, Lejeune, Sophie, Colas, Chrystelle, Buisine, Marie‐Pierre

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Identification of Rigosertib for the Treatment of Recessive Dystrophic Epidermolysis Bullosa-Associated Squamous Cell Carcinoma by Atanasova, Velina S, Pourreyron, Celine, Farshchian, Mehdi, Lawler, Michael, Brown, 4th, Christian A, Watt, Stephen A, Wright, Sheila, Warkala, Michael, Guttmann-Gruber, Christina, Hofbauer, Josefina Piñón, Fuentes, Ignacia, Prisco, Marco, Rashidghamat, Elham, Has, Cristina, Salas-Alanis, Julio C, Palisson, Francis, Hovnanian, Alain, McGrath, John A, Mellerio, Jemima E, Bauer, Johann W, South, Andrew P

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Glucosylated cholesterol in skin: Synthetic role of extracellular glucocerebrosidase by Boer, Daphne E.C., Mirzaian, Mina, Ferraz, Maria J., Nadaban, Andreea, Schreuder, Anne, Hovnanian, Alain, van Smeden, Jeroen, Bouwstra, Joke A., Aerts, Johannes M.F.G.

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Design and development of a series of borocycles as selective, covalent kallikrein 5 inhibitors by Walker, Ann L., Denis, Alexis, Bingham, Ryan P., Bouillot, Anne, Edgar, Emma V., Ferrie, Alan, Holmes, Duncan S., Laroze, Alain, Liddle, John, Fouchet, Marie-Helene, Moquette, Alexandre, Nassau, Pam, Pearce, Andrew C., Polyakova, Oxana, Smith, Kathrine J., Thomas, Pamela, Thorpe, James H., Trottet, Lionel, Wang, Yichen, Hovnanian, Alain

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Darier disease : A disease model of impaired calcium homeostasis in the skin by Savignac, Magali, Edir, Anissa, Simon, Marina, Hovnanian, Alain

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Reduced Intensity Conditioned Bone Marrow Transplant with Post-Transplant Cyclophosphamide and Donor-Derived Mesenchymal Stromal Cell Infusions for Recessive Dystrophic Epidermolys... by Ebens, Christen L., McGrath, John A, Tamai, Katsuto, Alain, Hovnanian, Wagner, John E., Riddle, Megan, Keene, Douglas R, DeFor, Todd E., Tryon, Rebecca, Chen, Mei, Woodley, David T, Hook, Kristin, Tolar, Jakub L

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KLK5 Inactivation Reverses Cutaneous Hallmarks of Netherton Syndrome: e1005389 by Furio, Laetitia, Pampalakis, Georgios, Michael, Iacovos P, Nagy, Andras, Sotiropoulou, Georgia, Hovnanian, Alain

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Kallikrein 5 inhibitors identified through structure based drug design in search for a treatment for Netherton Syndrome by White, Gemma V., Edgar, Emma V., Holmes, Duncan S., Lewell, Xiao Qing, Liddle, John, Polyakova, Oxana, Smith, Kathrine J., Thorpe, James H., Walker, Ann L., Wang, Yichen, Young, Robert J., Hovnanian, Alain

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Structure guided drug design to develop kallikrein 5 inhibitors to treat Netherton syndrome by Walker, Ann L., Bingham, Ryan P., Edgar, Emma V., Ferrie, Alan, Holmes, Duncan S., Liddle, John, Polyakova, Oxana, Rella, Monika, Smith, Kathrine J., Thorpe, James H., Wang, Yichen, White, Gemma V., Young, Robert J., Hovnanian, Alain

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Safety and early efficacy outcomes for lentiviral fibroblast gene therapy in recessive dystrophic epidermolysis bullosa by Lwin, Su M, Syed, Farhatullah, Di, Wei-Li, Kadiyirire, Tendai, Liu, Lu, Guy, Alyson, Petrova, Anastasia, Abdul-Wahab, Alya, Reid, Fiona, Phillips, Rachel, Elstad, Maria, Georgiadis, Christos, Aristodemou, Sophia, Lovell, Patricia A, McMillan, James R, Mee, John, Miskinyte, Snaigune, Titeux, Matthias, Ozoemena, Linda, Pramanik, Rashida, Serrano, Sonia, Rowles, Racheal, Maurin, Clarisse, Orrin, Elizabeth, Martinez-Queipo, Magdalena, Rashidghamat, Ellie, Tziotzios, Christos, Onoufriadis, Alexandros, Chen, Mei, Chan, Lucas, Farzaneh, Farzin, Del Rio, Marcela, Tolar, Jakub, Bauer, Johann W, Larcher, Fernando, Antoniou, Michael N, Hovnanian, Alain, Thrasher, Adrian J, Mellerio, Jemima E, Qasim, Waseem, McGrath, John A

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Corrigendum to ‘Design and development of a series of borocycles as selective, covalent kallikrein 5 inhibitors’ [Bioorg. Med. Chem. Lett. 29 (2019) 126675] by Walker, Ann L., Denis, Alexis, Bingham, Ryan P., Bouillot, Anne, Edgar, Emma V., Ferrie, Alan, Holmes, Duncan S., Laroze, Alain, Liddle, John, Fouchet, Marie-Helene, Moquette, Alexandre, Nassau, Pam, Pearce, Andrew C., Polyakova, Oxana, Smith, Kathrine J., Thomas, Pamela, Thorpe, James H., Trottet, Lionel, Wang, Yichen, Hovnanian, Alain

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Multidisciplinary care of epidermolysis bullosa during the COVID-19 pandemic—Consensus: Recommendations by an international panel of experts by Murrell, Dedee F., Lucky, Anne W., Salas-Alanis, Julio C., Woodley, David T., Palisson, Francis, Natsuga, Ken, Nikolic, Milos, Ramirez-Quizon, Mae, Paller, Amy S., Lara-Corrales, Irene, Barzegar, Mohammadreza Amir, Sprecher, Eli, Has, Cristina, Laimer, Martin, Bruckner, Anna L., Bilgic, Asli, Nanda, Arti, Purvis, Diana, Hovnanian, Alain, Murat-Sušić, Slobodna, Bauer, Johannes, Kern, Johannes S., Bodemer, Christine, Martin, Linda K., Mellerio, Jemima, Kowaleski, Cezary, Robertson, Susan J., Bruckner-Tuderman, Leena, Pope, Elena, Marinkovich, M. Peter, Tang, Jean Y., Su, John, Uitto, Jouni, Eichenfield, Lawrence F., Teng, Joyce, Aan Koh, Mark Jean, Lee, Sang Eun, Khuu, Phuong, Rishel, Heather I., Sommerlund, Mette, Wiss, Karen, Hsu, Chao-Kai, Chiu, Tor Wo, Martinez, Anna E.

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Loss of SPINK7 in Esophageal Epithelial Cells Unleashes a Pro-Inflammatory Response Characterized By Excessive Cytokine Production and Loss of Barrier Function by Azouz, Nurit Pereg, Michael, Demetria, Furio, Laetitia, Hovnanian, Alain, Rothenberg, Marc E., MD, PhD, FAAAAI

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Large-scale functional inference for skin-expressing lncRNAs using expression and sequence information by Patrick, Matthew T, Sreeskandarajan, Sutharzan, Shefler, Alanna, Wasikowski, Rachael, Sarkar, Mrinal K, Chen, Jiahan, Qin, Tingting, Billi, Allison C, Kahlenberg, J Michelle, Prens, Errol, Hovnanian, Alain, Weidinger, Stephan, Elder, James T, Kuo, Chao-Chung, Gudjonsson, Johann E, Tsoi, Lam C

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Deletions within COL7A1 Exons Distant from Consensus Splice Sites Alter Splicing and Produce Shortened Polypeptides in Dominant Dystrophic Epidermolysis Bullosa by Sakuntabhai, Anavaj, Hammami-Hauasli, Nadja, Bodemer, Christine, Rochat, Ariane, Prost, Catherine, Barrandon, Yann, de Prost, Yves, Lathrop, Mark, Wojnarowska, Fenella, Bruckner-Tuderman, Leena, Hovnanian, Alain

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Kallikrein-mediated proteolysis regulates the antimicrobial effects of cathelicidins in skin by Yamasaki, Kenshi, Schauber, Jürgen, Coda, Alvin, Lin, Henry, Dorschner, Robert A, Schechter, Norman M, Bonnart, Chrystelle, Descargues, Pascal, Hovnanian, Alain, Gallo, Richard L

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