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Contribution of Brain Intrinsic Branched-Chain Amino Acid Metabolism in a Novel Mouse Model of Maple Syrup Urine Disease
by
Kuhs, Amanda C
,
Ohl, Laura
,
Thurston, Tegan
,
Singh, Jeet
,
Bhuyan, Sangeetha
,
Grandinette, Sarah
,
Xu, Jing
,
Siemsgluess, Sophie A
,
Jakher, Youseff
,
Ahrens-Nicklas, Rebecca C
Published in
Journal of inherited metabolic disease
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Journal Title
Journal Of Inherited Metabolic Disease
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Subjects
3-Methyl-2-Oxobutanoate Dehydrogenase - Genetics
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3-Methyl-2-Oxobutanoate Dehydrogenase - Metabolism
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Amino Acids, Branched-Chain - Metabolism
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Animals
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Astrocytes - Metabolism
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Brain - Metabolism
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Disease Models, Animal
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Female
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Male
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Maple Syrup Urine Disease - Genetics
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Maple Syrup Urine Disease - Metabolism
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Mice
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Mice, Knockout
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Neurons - Metabolism
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Wiley-Blackwell Journals (Backfile Content)
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Springer Online Journals Archive Complete
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Springer Online Journals
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