Mitochondrial targets in hyperammonemia: Addressing urea cycle function to improve drug therapies by Moedas, Marco F., Simões, Ricardo J.M., Silva, Margarida F.B.

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Pathogenic SLC25A26 variants impair SAH transport activity causing mitochondrial disease by Schober, Florian A, Tang, Jia Xin, Sergeant, Kate, Moedas, Marco F, Zierz, Charlotte M, Moore, David, Smith, Conrad, Lewis, David, Guha, Nishan, Hopton, Sila, Falkous, Gavin, Lam, Amanda, Pyle, Angela, Poulton, Joanna, Gorman, Gráinne S, Taylor, Robert W, Freyer, Christoph, Wredenberg, Anna

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Stable Isotope Labeling of Amino Acids in Flies (SILAF) Reveals Differential Phosphorylation of Mitochondrial Proteins Upon Loss of OXPHOS Subunits by Rosenberger, Florian A., Atanassov, Ilian, Moore, David, Calvo-Garrido, Javier, Moedas, Marco F., Wedell, Anna, Freyer, Christoph, Wredenberg, Anna

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Quantitative proteomics of patient fibroblasts reveal biomarkers and diagnostic signatures of mitochondrial disease by Correia, Sandrina P, Moedas, Marco F, Taylor, Lucie S, Naess, Karin, Lim, Albert Z, McFarland, Robert, Kazior, Zuzanna, Rumyantseva, Anastasia, Wibom, Rolf, Engvall, Martin, Bruhn, Helene, Lesko, Nicole, Végvári, Ákos, Käll, Lukas, Trost, Matthias, Alston, Charlotte L, Freyer, Christoph, Taylor, Robert W, Wedell, Anna, Wredenberg, Anna

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The one-carbon pool controls mitochondrial energy metabolism via complex I and iron-sulfur clusters by Rosenberger, Florian A, Moore, David, Atanassov, Ilian, Moedas, Marco F, Clemente, Paula, Végvári, Ákos, Fissi, Najla El, Filograna, Roberta, Bucher, Anna-Lena, Hinze, Yvonne, The, Matthew, Hedman, Erik, Chernogubova, Ekaterina, Begzati, Arjana, Wibom, Rolf, Jain, Mohit, Nilsson, Roland, Käll, Lukas, Wedell, Anna, Freyer, Christoph, Wredenberg, Anna

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P-210 - Drug-induced effects on urea cycle enzymes associate with altered ammonia metabolism, NAD+ biosynthesis and mitochondrial protein acetylome by Moedas, Marco F, Farelo, Mafalda, Caio, João, Pereira, Antonina, IJlst, Lodewijk, Wanders, Ronald JA, Silva, Margarida FB

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Drug-induced effects on urea cycle enzymes associate with altered ammonia metabolism, NAD + biosynthesis and mitochondrial protein acetylome by Moedas, Marco F, Farelo, Mafalda, Caio, João, Pereira, Antonina, IJlst, Lodewijk, Wanders, Ronald JA, Silva, Margarida FB

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Transient decrease of hepatic NAD^sup +^ and amino acid alterations during treatment with valproate: new insights on drug-induced effects in vivo using targeted MS-based metabolomi... by Moedas, Marco F, van Cruchten, Arno G, Ijlst, Lodewijk, Kulik, Wim, de Almeida, Isabel Tavares, Diogo, Luísa, Wanders, Ronald J A, Silva, Margarida F B

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Transient decrease of hepatic NAD+ and amino acid alterations during treatment with valproate: new insights on drug-induced effects in vivo using targeted MS-based metabolomics by Moedas, Marco F., van Cruchten, Arno G., IJlst, Lodewijk, Kulik, Wim, de Almeida, Isabel Tavares, Diogo, Luísa, Wanders, Ronald J. A., Silva, Margarida F. B.

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Valproic acid utilizes the isoleucine breakdown pathway for its complete β-oxidation by Luís, Paula B.M., Ruiter, Jos P., Ofman, Rob, IJlst, Lodewijk, Moedas, Marco, Diogo, Luísa, Garcia, Paula, de Almeida, Isabel Tavares, Duran, Marinus, Wanders, Ronald J., Silva, Margarida F.B.

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