Patient-derived fibroblasts indicate oxidative stress status and may justify antioxidant therapy in OXPHOS disorders by Voets, A.M., Lindsey, P.J., Vanherle, S.J., Timmer, E.D., Esseling, J.J., Koopman, W.J.H., Willems, P.H.G.M., Schoonderwoerd, G.C., De Groote, D., Poll-The, B.T., de Coo, I.F.M., Smeets, H.J.M.

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Non-invasive versus ex vivo measurement of mitochondrial function in an endotoxemia model in rat: Toward monitoring of mitochondrial therapy by Wefers Bettink, Mark A., Harms, Floor A., Dollee, Nathalie, Specht, Patricia A.C., Raat, Nicolaas J.H., Schoonderwoerd, G.C., Mik, Egbert G.

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Molecular characterization of MPS IIIA, MPS IIIB and MPS IIIC in Tunisian patients by Deden, A.C., van Slegtenhorst, M.A., Ruijter, G.J.G., Schoonderwoerd, G.C., Huidekoper, H.H., Oussoren, E., Brooks, A.S., Demirdas, S.

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Physical Activity Is the Key Determinant of Skeletal Muscle Mitochondrial Function in Type 2 Diabetes by van Tienen, F. H. J, Praet, S. F. E, de Feyter, H. M, van den Broek, N. M, Lindsey, P. J, Schoonderwoerd, K. G. C, de Coo, I. F. M, Nicolay, K, Prompers, J. J, Smeets, H. J. M, van Loon, L. J. C

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A multi-center comparison of diagnostic methods for the biochemical evaluation of suspected mitochondrial disorders by Rodenburg, R J T, Schoonderwoerd, G C, Tiranti, V, Taylor, R W, Rötig, A, Valente, L, Invernizzi, F, Chretien, D, He, L, Backx, G P B M, Janssen, K J G M, Chinnery, P F, Smeets, H J, de Coo, I F, van den Heuvel, L P

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Brain abnormalities in a case of malonyl-CoA decarboxylase deficiency by de Wit, M.C.Y., de Coo, I.F.M., Verbeek, E., Schot, R., Schoonderwoerd, G.C., Duran, M., de Klerk, J.B.C., Huijmans, J.G.M., Lequin, M.H., Verheijen, F.W., Mancini, G.M.S.

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A simplified and reliable assay for complex I in human blood lymphocytes by de Wit, L.E.A., Spruijt, L., Schoonderwoerd, G.C., de Coo, I.F.M., Smeets, H.J.M., Scholte, H.R., Sluiter, W.

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