Glomangiopericytoma: An uncommon sinonasal perivascular tumor with particular characteristics

Glomangiopericytoma, sinonasal type hemangiopericytoma, is a rare sinonasal neoplasm with a perivascular myoid phenotype, and accounts for less than 0.5% of all sinonasal tumors. It is considered a distinct entity and differs from conventional soft-tissue hemangiopericytoma in location, clinical and...

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Bibliographic Details
Published in:Egyptian journal of ear, nose, throat and allied sciences nose, throat and allied sciences, 2011-11, Vol.12 (3), p.167-170
Main Authors: Chihani, Mehdi, Aljalil, Abdelfattah, Touati, Mohamed, Zoubeir, Youssef, Labraimi, Ahmed, Ammar, Haddou, Bouaity, Brahim
Format: Article
Language:English
Subjects:
Borderline tumor
Endoscopic resection
Glomangiopericytoma
Hemangiopericytoma
Histology
Nasal cavity
Nose
Surgery
Tumors
الأورام
الجراحة
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Summary:Glomangiopericytoma, sinonasal type hemangiopericytoma, is a rare sinonasal neoplasm with a perivascular myoid phenotype, and accounts for less than 0.5% of all sinonasal tumors. It is considered a distinct entity and differs from conventional soft-tissue hemangiopericytoma in location, clinical and histopathologic features. Glomangiopericytoma is a borderline low malignancy tumor with a good prognosis after complete surgical resection. We present the case of a 19-year-old girl presented with a progressive nasal obstruction, anosmia and epistaxis. Rhinoscopic examination and imaging studies showed a mass occupying the left nasal cavity without bone destruction. The tumor was removed successfully by endoscopic endonasal surgery. The anatomopathology examination with immunohistochemistry confirmed the diagnosis of glomangiopericytoma. In the light of this observation and a literature review, clinical aspects, histological characteristics, therapeutic principles and prognosis of this tumor will be discussed.
ISSN:2090-0740
2090-3405
DOI:10.1016/j.ejenta.2012.01.001