Hybrid procedure as a palliation approach in truncus arteriosus with interrupted aortic arch

Truncus arteriosus with interrupted aortic arch (Van Pragh A4) is a rare cyanotic heart disease. The management of this clinical entity is challenging due to obstructed systemic circulation, which required early intervention, especially in clinical setting with limited resources. Complete repair in...

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Bibliographic Details
Published in:Progress in pediatric cardiology 2020-03, Vol.56, p.101174, Article 101174
Main Authors: Mohsin, Muhammad, Ahmed, Waris, Karim, Farida, Sadqani, Saleem Akhtar
Format: Article
Language:English
Subjects:
Hybrid procedure
PDA stenting
Truncus arteriosus
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Summary:Truncus arteriosus with interrupted aortic arch (Van Pragh A4) is a rare cyanotic heart disease. The management of this clinical entity is challenging due to obstructed systemic circulation, which required early intervention, especially in clinical setting with limited resources. Complete repair in early neonatal period associated with high morbidity and mortality. We present two patients with truncus arteriosus (type A4) palliated with hybrid procedure previously reported for management of patients with hypoplastic left heart syndrome. •This case report gives insight into a treatment strategy for low income countries with limited resources for truncus arteriosus type A4 by adapting a palliation in neonatal period which was previously described for hypoplastic left heart syndrome.
ISSN:1058-9813
1558-1519
DOI:10.1016/j.ppedcard.2019.101174