Unsuccessful two-stage correction despite appropriate surgery in a case with disconnection (so-called absence) of the right pulmonaty artery

A right-sided modified Blalock-Taussig anastomosis was created using a 5 mm Gore-Tex tube in a 4½ month old infant with unilateral “absence” of the right pulmonary artery. Wide patency of the shunt was confirmed shortly after by angiography, but rarefaction of the peripheral right pulmonary arteries...

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Bibliographic Details
Published in:Cardiology in the young 1993-10, Vol.3 (4), p.445-447
Main Authors: Gildein, Hans P., von Bernuth, Götz, Mocellin, Rolf
Format: Article
Language:English
Subjects:
Absent pulmonary artery
Brief Reports
pulmonary vascular disease
surgery
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Summary:A right-sided modified Blalock-Taussig anastomosis was created using a 5 mm Gore-Tex tube in a 4½ month old infant with unilateral “absence” of the right pulmonary artery. Wide patency of the shunt was confirmed shortly after by angiography, but rarefaction of the peripheral right pulmonary arteries was seen at the age of 2½ years, when corrective surgery was performed. Postoperative hypoperfusion of the right lung, along with severe pulmonary vascular abnormalities seen in a lung biopsy, indicated failure of the two-stage correction in spite of appropriate surgery.
ISSN:1047-9511
1467-1107
DOI:10.1017/S104795110000192X