Malignant Pigmented Epithelioid Angiomyolipoma of the Kidney in a Child with Tuberous Sclerosis Complex

Introduction: Pigmented epithelioid angiomyolipoma is a variant of epithelioid angiomyolipoma (EAML) that has not previously been described in children with tuberous sclerosis. Case presentation: A 15-year-old boy with tuberous sclerosis had a rapidly enlarging renal mass associated with a left lung...

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Bibliographic Details
Published in:Fetal and pediatric pathology 2023-03, Vol.42 (2), p.285-290
Main Authors: Phan, Thu Dang Anh, To, Nhi Thuy, Pham, Diem Thi Nhu
Format: Article
Language:English
Subjects:
Adolescent
Angiomyolipoma - complications
Angiomyolipoma - diagnosis
Angiomyolipoma - pathology
Child
epithelioid angiomyolipoma
Epithelioid Cells - pathology
Humans
kidney
Kidney - pathology
Kidney Neoplasms - complications
Kidney Neoplasms - diagnosis
Kidney Neoplasms - pathology
Male
perivascular epithelioid cell neoplasms
Pigmented
Tuberous Sclerosis - complications
Tuberous Sclerosis - diagnosis
Tuberous Sclerosis - pathology
tuberous sclerosis complex
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Summary:Introduction: Pigmented epithelioid angiomyolipoma is a variant of epithelioid angiomyolipoma (EAML) that has not previously been described in children with tuberous sclerosis. Case presentation: A 15-year-old boy with tuberous sclerosis had a rapidly enlarging renal mass associated with a left lung nodule. Microscopically it was a pigmented EAML, confirmed by immunohistochemistry. Discussion/Conclusion: The pigmented variant of EAML can arise and metastasize from the kidney of a teenager with tuberous sclerosis.
ISSN:1551-3815
1551-3823
DOI:10.1080/15513815.2022.2088911