Agminated Fibroblastic Conective Tissue Nevus: A New Clinical Presentation

Connective tissue nevi are benign hamartomatous lesions in which one or several of the components of the dermis (collagen, elastin, glicosaminoglycans) show predominance or depletion. Recently, de Feraudy et al broadened the spectrum of connective tissue nevus, describing fibroblastic connective tis...

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Bibliographic Details
Published in:Pediatric dermatology 2016-07, Vol.33 (4), p.e240-e243
Main Authors: Downey, Camila, Requena, Luis, Bagué, Silvia, Sánchez Martínez, Miquel Ángel, Lloreta, Josep, Baselga, Eulalia
Format: Article
Language:English
Subjects:
Dermatofibrosarcoma - diagnosis
Diagnosis, Differential
Humans
Infant
Male
Nevus - diagnosis
Nevus - pathology
Nevus, Pigmented - pathology
Skin Neoplasms - pathology
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Summary:Connective tissue nevi are benign hamartomatous lesions in which one or several of the components of the dermis (collagen, elastin, glicosaminoglycans) show predominance or depletion. Recently, de Feraudy et al broadened the spectrum of connective tissue nevus, describing fibroblastic connective tissue nevus (FCTN), which is characterized by proliferation of CD34+ cells of fibroblastic and myofibroblastic lineage. Only solitary papules and nodules have been described. We present the first case of FCTN with multiple agminated lesions on the leg of an infant and the difficulties encountered in the differential diagnosis with dermatofibrosarcoma protuberans.
ISSN:0736-8046
1525-1470
DOI:10.1111/pde.12896