Pediatric split liver transplantation after F ontan procedure in left isomerism combined with biliary atresia: A case report

LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA . CHD can be associated with LI in up to 15% of cases, although it is rare in BA . Pediatric LT for a child with ESLD due to B...

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Bibliographic Details
Published in:Pediatric transplantation 2014-12, Vol.18 (8)
Main Authors: Youn, Joong Kee, Lee, Jeong‐Moo, Yi, Nam‐Joon, Choi, Young Rok, Suh, Suk‐Won, You, Tae, Lee, Kwang‐Woong, Jung, Chul‐Woo, Lee, Ji‐won, Bae, Eun‐Jung, Ko, Jae Sung, Kim, Woong‐Han, Park, Kwi‐Won, Suh, Kyung‐Suk
Format: Article
Language:English
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Summary:LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA . CHD can be associated with LI in up to 15% of cases, although it is rare in BA . Pediatric LT for a child with ESLD due to BA combined with LI and CHD is a challenging issue for a transplant surgeon. Herein, we report a successful split LT on a three‐yr‐old boy with LI who survived after a Fontan procedure due to single ventricle, but who suffered from HPS associated with BA .
ISSN:1397-3142
1399-3046
DOI:10.1111/petr.12364