Portal Vein Thrombosis of a Newborn with Corrected Total Anomalous Pulmonary Venous Return

• Published in: Turkish journal of haematology 2015-09, Vol.32 (3), p.267-270
• Main Authors: Çakır, Ufuk, Kahvecioğlu, Dilek, Alan, Serdar, Erdeve, Ömer, Atasay, Begüm, Uçar, Tayfun, Arsan, Saadet, Çakmaklı, Hasan, Ertem, Mehmet, Atalay, Semra
• Format: Article
• Language: English
• Subjects: Anticoagulants - therapeutic use; anticoagulation therapy; Cardiopulmonary Bypass - adverse effects; Case Report; Heart-Lung Machine - adverse effects; Heparin, Low-Molecular-Weight - therapeutic use; Humans; Hypothermia, Induced - adverse effects; Infant, Newborn; lowmolecular-weight heparin; Male; Portal Vein - diagnostic imaging; portal vein thrombosis; Postoperative Complications - diagnostic imaging; Postoperative Complications - drug therapy; Postoperative Complications - etiology; Scimitar Syndrome - surgery; total anomalous pulmonary venous return; Ultrasonography, Doppler; Venous Thrombosis - diagnostic imaging; Venous Thrombosis - drug therapy; Venous Thrombosis - etiology
• ISSN: 1300-7777; 1308-5263
• DOI: 10.4274/tjh.2013.0428

Total anomalous pulmonary venous return (TAPVR) is a rare and frequently isolated defect identified in 1% to 3% of all congenital heart diseases. To the best of our knowledge, portal vein thrombosis (PVT) associated with TAPVR has not been reported in the literature. We report a successfully managed PVT in a newborn with infracardiac-type TAPVR and review the literature. Anticoagulation therapies were used during the neonatal period to prevent thrombus progression. PVT should be kept in mind in TAPVR patients who have open heart repair with total correction. The treatment in each neonate should be individualized with consideration of the risk/benefit ratio.