Middle-Preserving Pancreatectomy for Multicentric Solid Pseudopapillary Neoplasm in a 10-Year-Old Female

Solid pseudopapillary neoplasm (SPN) is a rare low-grade malignant tumor of the pancreas that occurs predominantly in young females. This tumor is occasionally multicentric, posing a unique surgical conundrum for resection. We present a case of a 10-year-old female with a history of multicystic dysp...

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Bibliographic Details
Published in:European journal of pediatric surgery reports 2024-01, Vol.12 (1), p.e58-e62
Main Authors: Marshall, Grace, Byrne, Matthew, Wirth, Korry, Liao, Xiaoyan, Linehan, David C, Wilson, Nicole A
Format: Article
Language:English
Subjects:
Case Report
Frantz tumor
multicentric solid pseudopapillary neoplasm
pancreas
pediatric
urogenital abnormalities
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Summary:Solid pseudopapillary neoplasm (SPN) is a rare low-grade malignant tumor of the pancreas that occurs predominantly in young females. This tumor is occasionally multicentric, posing a unique surgical conundrum for resection. We present a case of a 10-year-old female with a history of multicystic dysplastic left kidney and persistent urogenital sinus who was diagnosed with biopsy-proven multicentric SPN of the pancreatic head and tail and underwent middle-preserving pancreatectomy. The patient tolerated the surgery very well. Our case is one of the few reported cases of multicentric SPN in a pediatric patient, and the only case treated with middle-preserving pancreatectomy, which is a novel surgical option for protecting pediatric patients from total endocrine and exocrine pancreatic insufficiency. With the increase in the incidence of SPN, there is an increasing need for pancreas-preserving surgical options, particularly in pediatric patients.
ISSN:2194-7619
2194-7627
DOI:10.1055/s-0044-1791812