Anaesthetic consideration in patients with Gorham′s syndrome: A case report and review of the literature

Gorham′s syndrome (GS) is a rare disorder characterized by proliferation of vascular channels resulting in destruction and resorption of osseous matrix leading to bone loss. Bone loss leads to joint instability and problems during airway management and positioning for surgery. Respiratory involvemen...

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Bibliographic Details
Published in:Indian journal of anaesthesia 2012, Vol.56 (4), p.391-393
Main Authors: Sahoo, RajendraKumar, Jagannathan, Balavenkatasubramanian, Palanichamy, Gurumoorthi, Natarajan, Vivekanand
Format: Article
Language:English
Subjects:
Airway management
anaesthesia
Gorham′s syndrome
spine surgery
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Summary:Gorham′s syndrome (GS) is a rare disorder characterized by proliferation of vascular channels resulting in destruction and resorption of osseous matrix leading to bone loss. Bone loss leads to joint instability and problems during airway management and positioning for surgery. Respiratory involvement further complicates anaesthesia management. We report the anaesthetic care of a 21-year-old male patient of known GS for spine decompression and fusion in prone position. Airway management, induction technique, pathophysiology of the disease, drug selection and other concerns of anaesthesia for major spine surgery has been discussed reviewing the sparse literature available.
ISSN:0019-5049
DOI:10.4103/0019-5049.100831