VATS therapy of chylothorax caused by leiomyomatosis complicated with tuberous sclerosis complex

Lymphangioleiomyomatosis with tuberous sclerosis complex is a rare disease. One of the most frequent complications of lymphangioleiomyomatosis is pleural effusion (chylothorax) wich can be treated with the use of VATS. Authors report a case of pulmonary lymphangioleiomyomatosis in a 56-year-old fema...

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Bibliographic Details
Published in:Journal of minimal access surgery 2013-04, Vol.9 (2), p.84-86
Main Authors: Csiszkó, Adrienn, Herr, György, Sz. Kiss, Sándor, Hallay, Judit, Gyöngyösi, Zoltán, Szentkereszty, Zsolt
Format: Article
Language:English
Subjects:
Care and treatment
Case studies
Causes of
Chylothorax
Complications and side effects
Diagnosis
Health aspects
Leiomyoma
lymphangioleiomyomatosis
Patient outcomes
Thoracic surgery
Thoracoscopy
Tuberous sclerosis
tuberous sclerosis complex
Tumors
Unusual Case
Videothoracoscopy
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Summary:Lymphangioleiomyomatosis with tuberous sclerosis complex is a rare disease. One of the most frequent complications of lymphangioleiomyomatosis is pleural effusion (chylothorax) wich can be treated with the use of VATS. Authors report a case of pulmonary lymphangioleiomyomatosis in a 56-year-old female patient with tuberous sclerosis complex with an 8-week history of recurrent chylothorax, dyspnea and debilitating weakness. By CT scan a flat tissue proliferation was seen in the site of the thoracic duct and it was supposed to be the reason for the pleural effusion. A VATS resection of this laesion and ligation of the thoracic duct was performed successfully. Chylothorax is often associated with pulmonary lymphangioleiomyomatosis. Lymphangioleiomyomatosis combined with tuberous sclerosis complex is extremely rare. In case of chylothorax VATS treatment is successful and may be the first choice.
ISSN:0972-9941
1998-3921
DOI:10.4103/0972-9941.110970