Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma

We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-...

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Bibliographic Details
Published in:Frontiers in cardiovascular medicine 2021-10, Vol.8
Main Authors: Cossío-Aranda, Jorge, Aranda-Frausto, Alberto, Berarducci, Joaquin, Espinola-Zavaleta, Nilda, González-Melchor, Laila, Vázquez-Antona, Clara, Meléndez-Ramirez, Gabriela, Armenta-Moreno, Javier Ivan, Keirns, Candace
Format: Article
Language:English
Subjects:
arrhythmia
cardiac tumor
cardiooncology
Cardiovascular Medicine
PEComa
perivascular epithelioid cell neoplasm
rhabdomyoma of heart
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Summary:We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.”
ISSN:2297-055X
2297-055X
DOI:10.3389/fcvm.2021.709328