PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature

Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemo...

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Bibliographic Details
Published in:Case Reports in Medicine 2013-01, Vol.2013 (2013), p.113-116-229
Main Authors: Khaja, Faseeh, Carilli, Allison, Baidas, Said, Sriharan, Aravindhan, Norford, Shanedelle
Format: Article
Language:English
Subjects:
Care and treatment
Case Report
Case studies
Causes of
Development and progression
Diagnosis
Epithelial tumors
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Summary:Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemotherapy including mTOR inhibitors for malignant tumors. Here we discuss the radiological and pathological diagnosis, evaluation, and management of a hepatic PEComa. We describe a 51-year-old patient who was diagnosed incidentally after unusual physical exam findings.
ISSN:1687-9627
1687-9635
DOI:10.1155/2013/904126