Chiari Malformation-I with Syringomyelia: A Non-specific Presentation and Surgical Consideration

Chiari Malformation-I is a congenital disorder characterized by the anatomical defect of the base of skull with tonsillar herniation (≥5 mm) below the foramen magnum, which is detected on MRI. It has a diverse range of symptoms with non-specific presentation leading to the chances of misdiagnosis an...

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Bibliographic Details
Published in:Nepal journal of neuroscience 2016-12, Vol.13 (2), p.105-108
Main Authors: Maharjan, Jemesh S, Shrestha, Pranaya, Chandra, Avinash, Rajbhandari, Pravesh, Acharya, Samir, Shrestha, Resha, Bhattarai, Robin, Pant, Basant
Format: Article
Language:English
Subjects:
chiari malformation-i
posterior fossa decompression
syringo-subarachnoid shunt
syringomyelia
tonsillar herniation
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Summary:Chiari Malformation-I is a congenital disorder characterized by the anatomical defect of the base of skull with tonsillar herniation (≥5 mm) below the foramen magnum, which is detected on MRI. It has a diverse range of symptoms with non-specific presentation leading to the chances of misdiagnosis and untimely recognition of the disorder. Syringomyelia is the most common result of Chiari-I. The selection of surgical or non-surgical management depends upon the patient symptoms and the presence of absence of Syringomyelia. The objective of this case report is to give a broad perspective on Chiari Malformation-I from the symptoms and clinical findings obtained in a patient with Syringomyelia associated with Chiari Malformation-I and to discuss about the different surgical options as well as the psychological support required for the management of the condition.Nepal Journal of Neuroscience. Vol. 13, No. 2, 2016, Page: 105-108 
ISSN:1813-1948
1813-1956
DOI:10.3126/njn.v13i2.20489