Biological encirclage-Traboulsi syndrome

Traboulsi syndrome is a sporadic autosomal recessive disorder. Very few cases reported and no surgical treatment has been described. The purpose of the study was to describe the surgical treatment of a case of Traboulsi syndrome with intercalary staphyloma. Traboulsi syndrome[1-3] is a type of spont...

Full description

Saved in:
Bibliographic Details
Published in:Indian journal of ophthalmology 2024-07, Vol.72 (7), p.1075-1075
Main Authors: Beniwal, Abhijeet, Bafna, Rahul Kumar, Roop, Prakhyat, Lata, Suman, Sharma, Namrata
Format: Article
Language:English
Subjects:
Adult
Anterior chamber
Anterior Chamber - surgery
biological encirclage
Cornea
cross-linked cornea
Female
Hereditary diseases
Humans
IJO Video
Intraocular Pressure - physiology
Lens Subluxation - diagnosis
Lens Subluxation - surgery
Ophthalmologic Surgical Procedures - methods
staphyloma
Suture Techniques
Sutures
Syndrome
traboulsi syndrome
tuck in keratoplasty
Visual Acuity
Citations: Items that this one cites
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Traboulsi syndrome is a sporadic autosomal recessive disorder. Very few cases reported and no surgical treatment has been described. The purpose of the study was to describe the surgical treatment of a case of Traboulsi syndrome with intercalary staphyloma. Traboulsi syndrome[1-3] is a type of spontaneous filtering bleb. The case was of a 31-year-old lady with a flat anterior chamber and large intercalary staphyloma, with a subluxated clear lens. Liberal peritomy was done. The staphyloma was cut and the displaced lens was delivered through it. It was closed with 7-0 vicryl continuous suture. A cross-linked cornea was used after removing the Descemet membrane. It was modified to match the crescentic shape of the limbus by using 11 and 6 mm trephine. Two wedge-shaped defects were created and tissue was excised between them, which were then sutured to increase the arc radius. A peripheral flange at the corneal edge was created. A pocket was created in the host cornea to accommodate the donor corneal flange. The donor cornea was tucked in and the graft was sutured. The sclera was used to suture another side prophylactically, making a 360-degree encirclage. The patient got ambulatory vision postsurgery. The use of the cornea as biological encirclage has not been described previously. Using a cross-linked cornea. Creating wedge-shaped defects in crescentic corneal graft to increase arc radius. Use of cornea as encirclage.Link of video:https://youtu.be/T3b5rkvFmlc.
ISSN:0301-4738
1998-3689
1998-3689
DOI:10.4103/IJO.IJO_1968_23