Kartagener syndrome

Kartagener Syndrome is an autosomal recessive disorder, a subgroup of primary ciliary dyskinesia, characterized by a triad of bronchiectasis, sinusitis and situs inversus. In cases of recurrent lower respiratory tract infections Kartagener syndrome should be kept in mind to prevent unnecessary repea...

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Bibliographic Details
Published in:Gomal journal of medical sciences 2014-07, Vol.11 (2)
Main Authors: Babar, Khalid Shakeel, Khan, Habibullah, Ismail, Yasser, Azim, Qaisar, Fawad, Muhammad
Format: Article
Language:English
Subjects:
bronchiectasis
Care and treatment
Case studies
dextrocardia
Diagnosis
Kartagener syndrome
sinusitis
situs inversus
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Summary:Kartagener Syndrome is an autosomal recessive disorder, a subgroup of primary ciliary dyskinesia, characterized by a triad of bronchiectasis, sinusitis and situs inversus. In cases of recurrent lower respiratory tract infections Kartagener syndrome should be kept in mind to prevent unnecessary repeated admissions, investigations and inappropriate treatment. Social, psychological and fertility issues should be addressed once it is diagnosed to help these patients to live with Kartagener syndrome safely. Here we present a case of 37 year old female who presented with bronchiectasis, recurrent episodes of sinusitis and situs inversus which conforms to the triad of Kartagener syndrome.
ISSN:1819-7973
1997-2067