The fatty spleen: Severe hypertriglyceridemia leading to splenomegaly in a child

Abstract This report describes a 3-year-old male with splenomegaly that presented as an infant with pancreatitis, a pancreatic pseudocyst, and a liver nodule. The patient underwent prophylactic splenectomy at age 3 years due to rapid enlargement and increasing risk for traumatic hemorrhage. Patholog...

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Bibliographic Details
Published in:Journal of pediatric surgery case reports 2017-02, Vol.17 (C), p.25-27
Main Authors: Kniery, Kevin R, Kay, Jeffrey T, Escobar, Mauricio A
Format: Article
Language:English
Subjects:
Hypertriglyceridemia
Lipoprotein lipase deficiency
Pediatric lipid disorders
Splenectomy
Splenomegaly
Surgery
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Summary:Abstract This report describes a 3-year-old male with splenomegaly that presented as an infant with pancreatitis, a pancreatic pseudocyst, and a liver nodule. The patient underwent prophylactic splenectomy at age 3 years due to rapid enlargement and increasing risk for traumatic hemorrhage. Pathology revealed lipid-laden histiocytes rather than stigmata of the expected diagnosis of sinistral hypertension from splenic vein thrombosis.
ISSN:2213-5766
2213-5766
DOI:10.1016/j.epsc.2016.12.001