Biphasic renal synovial sarcoma with extensive venous tumor thrombosis: A rare presentation

Primary renal synovial sarcoma (SS) is a very rare soft-tissue tumor arising from the kidney. These tumors histologically closely resemble other sarcoma variants. Immunohistochemical and cytogenetic techniques remain the cornerstone in achieving the correct diagnosis. Radical surgical excision is th...

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Bibliographic Details
Published in:Urology annals 2018-07, Vol.10 (3), p.339-341
Main Authors: Dutt, Uma, Manikandan, Ramanathinam, Dorairajan, Lalgudi, Srinivas, Bheemanathi
Format: Article
Language:English
Subjects:
Adjuvant chemotherapy
Blood clots
Case Report
Chemotherapy
Chromosomes
Cytogenetics
Diagnosis
Histology
Histopathology
immunohistochemistry
Medical imaging
Medical prognosis
Metastasis
Patients
renal synovial sarcoma
Sarcoma
Synovial sarcoma
Thrombosis
Tumors
Veins & arteries
venous tumor thrombosis
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Summary:Primary renal synovial sarcoma (SS) is a very rare soft-tissue tumor arising from the kidney. These tumors histologically closely resemble other sarcoma variants. Immunohistochemical and cytogenetic techniques remain the cornerstone in achieving the correct diagnosis. Radical surgical excision is the primary treatment for local tumor control and alleviation of symptoms. Adjuvant chemotherapy, at present, has only a limited role. We report a unique case of a 21-year-old young male with the diagnosis of a biphasic renal SS with extensive venous system thrombosis involving the inferior vena cava, bilateral iliac, and femoral vessels which was managed by radical nephrectomy and tumor thrombectomy followed by adjuvant chemotherapy.
ISSN:0974-7796
0974-7834
DOI:10.4103/UA.UA_9_18