Tracheobronchomegaly as a Cause of Bronchiectasis in an Adult

Mounier-Kuhn syndrome (MKS) is a rare congenital anomaly characterized by dilated trachea and main bronchi due to atrophy of the elastic fibers and smooth muscle cells of the trachea and major airways. Patients of MKS can have varied presentation. The diagnosis is established radiologically and bron...

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Bibliographic Details
Published in:Case reports in pulmonology 2016-01, Vol.2016 (2016), p.1-4
Main Authors: Narayanasami, Suryakala, Nagamalli Kumar, Balla, Mohanty Mohapatra, Madhusmita, Govindaraj, Vishnukanth
Format: Article
Language:English
Subjects:
Case Report
Diagnosis
Genetic disorders
Health aspects
Infections
Patients
Respiratory tract diseases
Tomography
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Summary:Mounier-Kuhn syndrome (MKS) is a rare congenital anomaly characterized by dilated trachea and main bronchi due to atrophy of the elastic fibers and smooth muscle cells of the trachea and major airways. Patients of MKS can have varied presentation. The diagnosis is established radiologically and bronchoscopically. There is no specific treatment for MKS. We present an adult man with MKS who presented with recurrent respiratory tract infection. The diagnosis was confirmed by imaging study and fiberoptic bronchoscopy.
ISSN:2090-6846
2090-6854
DOI:10.1155/2016/5049406