Isolation of the left innominate artery: When to operate?

A right aortic arch with an isolated left innominate artery from the pulmonary artery is an exceedingly rare congenital cardiac malformation. We describe the management and complex surgical timing considerations in two such cases, successfully operated on day 4 and 7 months of age, including the use...

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Bibliographic Details
Published in:Annals of pediatric cardiology 2024-01, Vol.17 (1), p.74-76
Main Authors: Parsons, Samuel J H, Nuttall, Harry, Jones, Alexander
Format: Article
Language:English
Subjects:
Care and treatment
Case Report
Congenital heart disease
cranial ultrasound
Diagnosis
Genetic disorders
isolated innominate artery
lef1 gene
Pediatric cardiology
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Description
Summary:A right aortic arch with an isolated left innominate artery from the pulmonary artery is an exceedingly rare congenital cardiac malformation. We describe the management and complex surgical timing considerations in two such cases, successfully operated on day 4 and 7 months of age, including the use of cranial ultrasound as a helpful tool to guide decision-making. We also describe the first reported association of this defect with a 4q25 deletion encompassing the gene.
ISSN:0974-2069
0974-5149
DOI:10.4103/apc.apc_191_23