Familial mediterranean fever and immunoglobulin A nephropathy: A case report and review of the literature

Familial Mediterranean fever (FMF) is an autosomal recessive disease charac-terized by recurrent fever episodes and polyserositis. The most important complication is amyloidosis. Nonamyloidotic nephropathy in FMF is poorly documented. Besides amyloidosis, different types of glomerulonephritis may ra...

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Bibliographic Details
Published in:Saudi journal of kidney diseases and transplantation 2020-03, Vol.31 (2), p.537-541
Main Authors: Keles, Meryem, Yilmaz, Fatih
Format: Article
Language:English
Subjects:
Acute Kidney Injury - etiology
Amyloidosis
Anti-Inflammatory Agents - therapeutic use
Biopsy
Care and treatment
Case reports
Colchicine
Colchicine - therapeutic use
Diseases
Drug dosages
Familial Mediterranean Fever - complications
Familial Mediterranean Fever - diagnosis
Familial Mediterranean Fever - drug therapy
Fever
Genetic aspects
Glomerulonephritis
Glomerulonephritis, IGA - diagnosis
Glomerulonephritis, IGA - drug therapy
Glomerulonephritis, IGA - etiology
Glucocorticoids - therapeutic use
Gout suppressants
Hematuria
Hematuria - etiology
Humans
Immunoglobulin A
Immunoglobulins
Kidney diseases
Laboratories
Male
Mutation
Patients
Periodic disease
Prednisolone - therapeutic use
Proteins
Proteinuria - etiology
Treatment Outcome
Urine
Young Adult
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Description
Summary:Familial Mediterranean fever (FMF) is an autosomal recessive disease charac-terized by recurrent fever episodes and polyserositis. The most important complication is amyloidosis. Nonamyloidotic nephropathy in FMF is poorly documented. Besides amyloidosis, different types of glomerulonephritis may rarely be seen in FMF patients. A 24-year-old male patient followed up due to FMF was evaluated for macroscopic hematuria and acute kidney injury. The patient was diagnosed as immunoglobulin A nephropathy with renal biopsy. The patient gave a good response to colchicine and steroid treatment. The case reports in the literature about the treatment of the patients with association of FMF and glomerulonephritis are insufficient, and there are no satisfactory epidemiological and treatment outcome reports.
ISSN:1319-2442
2320-3838
DOI:10.4103/1319-2442.284033