Undifferentiated duodenal sarcoma with rhabdoid features

Tumors of the pediatric gastrointestinal tract are uncommon, with duodenal malignancies being extremely rare. Malignant rhabdoid tumor is a rare highly aggressive tumor that occurs in young children with a very poor clinical outcome. The tumor is characterized by a diffuse proliferation of “rhabdoid...

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Bibliographic Details
Published in:Journal of pediatric surgery case reports 2020-07, Vol.58, p.101451, Article 101451
Main Authors: Karkera, Parag J., Bendre, Pradnya S.
Format: Article
Language:English
Subjects:
Duodenal
Malignant rhabdoid tumour
Undifferentiated
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Description
Summary:Tumors of the pediatric gastrointestinal tract are uncommon, with duodenal malignancies being extremely rare. Malignant rhabdoid tumor is a rare highly aggressive tumor that occurs in young children with a very poor clinical outcome. The tumor is characterized by a diffuse proliferation of “rhabdoid cells,” which are round or polygonal with eccentric nuclei, prominent nucleoli, and glassy eosinophilic cytoplasm containing hyaline-like inclusion bodies. Very few cases of malignant tumors with rhabdoid features of the gastrointestinal tract are described in literature, but probably none so far in the duodenum of a pediatric patient. We present a case of a eleven year old with an undifferentiated tumour of the duodenum with rhabdoid features on histopathology, who underwent multimodality management and is doing well at 1 year of follow up.
ISSN:2213-5766
2213-5766
DOI:10.1016/j.epsc.2020.101451