Synovial Sarcoma of Ethmoidal Sinus

Abstract Background  Synovial sarcoma is an aggressive soft tissue cancer of extremities mainly and rare in head and neck region, whereas rarest in ethmoidal sinus as only three cases have been reported till date. Case Reports  We managed two cases of synovial sarcoma who presented with nasal obstru...

Full description

Saved in:
Bibliographic Details
Published in:Surgery journal (New York) 2021-07, Vol.7 (3), p.e195-e198
Main Authors: Dhiman, Sapna, Negi, Sarita, Moudgil, Sandeep, Thakur, Jagdeep S., Azad, Ramesh K.
Format: Article
Language:English
Subjects:
Case Report
ethmoid sinus
nose
synovial sarcoma
tumor
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Abstract Background  Synovial sarcoma is an aggressive soft tissue cancer of extremities mainly and rare in head and neck region, whereas rarest in ethmoidal sinus as only three cases have been reported till date. Case Reports  We managed two cases of synovial sarcoma who presented with nasal obstruction, epistaxis, and swelling around the nasofacial region. Endoscopic nasal biopsy and immunohistochemistry markers confirmed synovial sarcoma in both the cases. While one case was managed by surgery and chemoradiation, the second patient received two cycles of ifosfamide-based chemotherapy and succumbed after 6 weeks of diagnosis. Conclusion  Head and neck sarcomas are aggressive and carry a poor prognosis. Surgical resection with postoperative radiotherapy is the standard treatment. However, they have a high risk of recurrence and hence aggressive management and close follow-up is warranted for the optimal outcome.
ISSN:2378-5128
2378-5136
DOI:10.1055/s-0041-1731634