Complete form of pachydermoperiostosis

Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is repo...

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Bibliographic Details
Published in:Anais brasileiros de dermatología 2020-01, Vol.95 (1), p.98-101
Main Authors: Honório, Mônica Larissa Padilha, Bezerra, Guilherme Holanda, Costa, Vivianne Lira da Câmara
Format: Article
Language:English
Subjects:
Adolescent health
DERMATOLOGY
Erythema - pathology
Heredity
Humans
Images in Dermatology
Male
Osteoarthropathy
Osteoarthropathy, Primary Hypertrophic - pathology
Primary hypertrophic
Scalp Dermatoses - pathology
Young Adult
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Summary:Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is reported in a male patient with disease onset in adolescence, with compatible clinical and radiological findings, presenting the three cardinal findings as well as other associated manifestations, such as hyperhidrosis and acne.
ISSN:0365-0596
1806-4841
1806-4841
DOI:10.1016/j.abd.2019.04.009