Medial canthal lesions in a man with a scarred wrist: Subcutaneous lymphangiomas in association with Maffucci’s syndrome

Maffucci syndrome is characterized by multiple soft tissue hemangiomas and multiple enchondromas. Ollier disease includes enchondromatosis without hemangiomas and these two conditions are now thought to represent a spectrum of congenital mesenchymal dysplasia. We present a case of a 49 year-old male...

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Bibliographic Details
Published in:Vision Pan-America 2014-01, Vol.13 (1), p.13-15
Main Authors: Valenzuela, Alejandra A, J Godfrey Heathcote
Format: Article
Language:English
Subjects:
Case reports
lymphangiomas, Maffucci’s syndrome, enchondromas, Ollier syndrome
Online Access:Get full text
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Summary:Maffucci syndrome is characterized by multiple soft tissue hemangiomas and multiple enchondromas. Ollier disease includes enchondromatosis without hemangiomas and these two conditions are now thought to represent a spectrum of congenital mesenchymal dysplasia. We present a case of a 49 year-old male affected by multiple enchondromas, who was reclassified as a Maffucci lymphangioma syndrome after two periocular lymphangiomas were surgically excised.
ISSN:2219-4665
2219-4673
DOI:10.15324/vpa.v13i1.66