Reducing the Burden of Care: Multidisciplinary Management of Late-Manifested Crouzon Syndrome-A Case Report

The therapy of patients with Crouzon syndrome involves a multidisciplinary team. In most cases, this therapy is extensive, time-consuming, and exhausting for the patient. This case report illustrates a temporally coordinated therapy plan that succeeds in reducing the burden of care. Showing typical...

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Bibliographic Details
Published in:Children (Basel) 2021-12, Vol.8 (12), p.1122
Main Authors: Achterrath, Sarah, Kruse, Teresa, Neuschulz, Julia, Graf, Isabelle, Zöller, Joachim, Braumann, Bert
Format: Article
Language:English
Subjects:
Birth defects
burden of care
Case Report
Case reports
Crouzon syndrome
Intracranial pressure
Magnetic resonance imaging
Medical personnel
midface advancement
Mutation
Oral hygiene
Orthodontics
Patients
Pediatrics
Quality of life
Questionnaires
Retention
Surgery
Sutures
systemic acceleratory phenomenon
treatment planning
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Summary:The therapy of patients with Crouzon syndrome involves a multidisciplinary team. In most cases, this therapy is extensive, time-consuming, and exhausting for the patient. This case report illustrates a temporally coordinated therapy plan that succeeds in reducing the burden of care. Showing typical extraoral characteristics of Crouzon syndrome, the patient had a frontal and left-sided crossbite, and impaction of the maxillary canines. Multidisciplinary therapy included the extraction of multiple teeth, midface distraction at Le Fort III level, and alignment of the impacted teeth. Before starting, during, and after completion of the treatment, the patient's oral health-related quality of life was assessed using COHIP-19. The combination of different treatment steps significantly reduced the duration of therapy. The therapy improved not only the patient's oro- and craniofacial function, but also the patient's facial appearance in a short treatment period. The patient's quality of life improved considerably during this time. In the treatment of severe craniofacial anomalies, the highest priority should be given to keeping the burden of care low. All measures should encourage young patients' appropriate psychosocial development despite extensive therapies, ensuring at the same time medically satisfactory treatment results.
ISSN:2227-9067
2227-9067
DOI:10.3390/children8121122