Linear scleroderma and primary sclerosing cholangitis: An undescribed association

Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a pa...

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Bibliographic Details
Published in:Indian journal of dermatology 2020-11, Vol.65 (6), p.514-515
Main Authors: Fernández, Iñigo, Alonso, Susana, Vian, Carlos, Del Cura, L, González-Vela, Carmen, González-López, Marcos
Format: Article
Language:English
Subjects:
Bile
Case Report
Case reports
Cholangitis
Comorbidity
linear scleroderma
Liver
Liver diseases
morphea
Pathology
primary sclerosing cholangitis
Scleroderma
Scleroderma (Disease)
Skin
Skin diseases
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Summary:Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease.
ISSN:0019-5154
1998-3611
DOI:10.4103/ijd.IJD_473_18