Erythema Gyratum Repens-Like Purpura in a Patient with Sjögren Syndrome

The etiology of purpura in Sjögren syndrome (SS) includes cryoglobulinemia, hypergammaglobulinemia, and leukocytoclastic vasculitis (LCV). The clinical symptoms of LCV associated with SS comprise palpable or nonpalpable purpura and urticarial vasculitis. Here, we report a case of LCV presenting as e...

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Bibliographic Details
Published in:Case reports in dermatology 2017-06, Vol.9 (2), p.40-43
Main Authors: Fukunaga, Miyuki, Harada, Kazutoshi, Mae, Kenichiro, Wakamatsu, Kanae, Kiriyama, Noriko, Tsuboi, Ryoji, Okubo, Yukari
Format: Article
Language:English
Subjects:
Annular erythema
Case reports
Dermatology
Hypergammaglobulinemia
Laboratories
Leukocytoclastic vasculitis
Purpura
Rheumatoid arthritis
Single Case
Sjögren syndrome
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Summary:The etiology of purpura in Sjögren syndrome (SS) includes cryoglobulinemia, hypergammaglobulinemia, and leukocytoclastic vasculitis (LCV). The clinical symptoms of LCV associated with SS comprise palpable or nonpalpable purpura and urticarial vasculitis. Here, we report a case of LCV presenting as erythema gyratum repens (EGR)-like purpura in a 62-year-old woman with rheumatoid arthritis and SS. EGR-like skin lesions, characterized by annular lesions with expanding concentric pattern and coalescing to form a zebra-like pattern or grain of wood pattern, can appear in various autoimmune conditions; however, EGR-like eruption in SS is extremely rare. On the basis of the expansion pattern, we considered that the EGR-like purpura in this case was elicited by urticarial vasculitis accompanied by SS.
ISSN:1662-6567
1662-6567
DOI:10.1159/000477375