Unique presentation of recurrent subdural effusions and subsequent abdominal lymphadenopathy in a patient diagnosed with Kikuchi-Fujimoto disease

Kikuchi Fujimoto Disease, originally discovered in 1972, is a rare lymphoproliferative disorder traditionally characterized by cervical lymphadenopathy, fevers, parotid gland enlargement, and several other nonspecific manifestations. Differentials include lymphoma, other viral diseases such as Epste...

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Bibliographic Details
Published in:Radiology case reports 2022-04, Vol.17 (4), p.1163-1168
Main Authors: Rana, Gaurav, Awad, Ahmed, Wang, Edwin, Webb, Shaun, Zahir, Haziq, Ree, Alexander
Format: Article
Language:English
Subjects:
Case Report
Histiocytic Necrotizing Lymphadenitis
IgG4 related-disease
Kaposi Sarcoma
Kikuchi Fujimoto disease
Lymphadenopathy
Lymphoproliferative disorder
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Summary:Kikuchi Fujimoto Disease, originally discovered in 1972, is a rare lymphoproliferative disorder traditionally characterized by cervical lymphadenopathy, fevers, parotid gland enlargement, and several other nonspecific manifestations. Differentials include lymphoma, other viral diseases such as Epstein-Bar Virus, as well as other autoimmune conditions such as Systemic Lupus Erythematosus. Central nervous system involvement is exceptionally rare, with manifestations including meningitis as well as subdural effusions, as presented in this case. This review will summarize a case of a 24-year-old man with recurrent subdural effusions requiring intervention, subsequent relapse with abdominal lymphadenopathy, and possible IgG4 related disease. The background epidemiology, radiology, and potential pathophysiology will be reviewed.
ISSN:1930-0433
1930-0433
DOI:10.1016/j.radcr.2021.12.049