Transposition of the great arteries with total anomalous pulmonary venous connection in a 1½year-old child: Pulmonary arterial hypertension - An advantage

Transposition of the great arteries with total anomalous pulmonary venous connection is a rare anomaly with varied management approach depending on the time of presentation; the management of cases which present early is usually by anatomical surgical approach while late presentation is by physiolog...

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Bibliographic Details
Published in:Annals of pediatric cardiology 2021-04, Vol.14 (2), p.235-238
Main Authors: Abah, Rose, Prabhu, Atul, Katewa, Ashish, Sahu, Balswaroop
Format: Article
Language:English
Subjects:
anatomic correction
Case Report
pulmonary arterial hypertension
Pulmonary hypertension
total anomalous pulmonary venous connection
transposition of the great arteries
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Summary:Transposition of the great arteries with total anomalous pulmonary venous connection is a rare anomaly with varied management approach depending on the time of presentation; the management of cases which present early is usually by anatomical surgical approach while late presentation is by physiologic approach. This is due to early left ventricular mass regression as a result of the absence of volume and pressure load to the left ventricle (LV). We report a late presentation (at 1½ years of age) that had a successful anatomic surgical correction because the LV was "prepared" by both pressure and volume load from pulmonary arterial hypertension and large ostium secundum atrial septal defect.
ISSN:0974-2069
0974-5149
DOI:10.4103/apc.APC_65_20