Diagnostic dilemma in diagnosing rare cause of protein losing enteropathy: Waldmann's disease

Waldmann's disease, or primary intestinal lymphangiectasia, is an unusual cause of protein‐losing enteropathy primarily characterized by lymphopenia, hypoalbuminemia, and hypogammaglobulinemia. However, variable clinical presentations result dilemmas in diagnosis and effective management. We pr...

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Bibliographic Details
Published in:Clinical case reports 2022-06, Vol.10 (6), p.e5992-n/a
Main Authors: Prajapati, Sarita, Bohara, Sujan, Mainali, Gaurab, Karki, Samikshya, Thapa, Sharan, Aryal, Nirjala
Format: Article
Language:English
Subjects:
Abdomen
Anemia
Ascites
Biopsy
Case Report
Case Reports
Congenital diseases
Diet
Disease
Edema
Endoscopy
intestinal lymphangiectasia
Iron
Localization
Lymphatic system
medium‐chain triglycerides
Proteins
protein‐losing enteropathy
Small intestine
Triglycerides
Waldmann's disease
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Summary:Waldmann's disease, or primary intestinal lymphangiectasia, is an unusual cause of protein‐losing enteropathy primarily characterized by lymphopenia, hypoalbuminemia, and hypogammaglobulinemia. However, variable clinical presentations result dilemmas in diagnosis and effective management. We present a toddler diagnosed with Waldmann's disease managed with a high‐protein diet and medium‐chain triglyceride supplementation. Waldmann's disease, or primary intestinal lymphangiectasia, is an unusual cause of protein‐losing enteropathy primarily characterized by lymphopenia, hypoalbuminemia, and hypogammaglobulinemia. However, variable clinical presentations result in dilemmas in diagnosis and effective management.
ISSN:2050-0904
2050-0904
DOI:10.1002/ccr3.5992