Laparoscopic resection of pheochromocytoma (paraganglioma) of the organ of Zuckerkandl in a pediatric patient

AbstractBackgroundPheochromocytoma is a rare neuroendocrine tumor that secretes catecholamines. Classically located in the adrenal gland, a small percentage of pheochromocytomas arise along the sympathetic chain. The majority of cases are diagnosed among adults age 20–50 years old. Laparoscopic adre...

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Bibliographic Details
Published in:Journal of pediatric surgery case reports 2022-02, Vol.77, p.102165-102165, Article 102165
Main Authors: Kramme, Katherine, Fountain, Robin, Leinwand, Michael
Format: Article
Language:English
Subjects:
Extra-adrenal pheochromocytoma
Laparoscopy
Minimally invasive
Neuroendocrine tumor
Surgery
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Summary:AbstractBackgroundPheochromocytoma is a rare neuroendocrine tumor that secretes catecholamines. Classically located in the adrenal gland, a small percentage of pheochromocytomas arise along the sympathetic chain. The majority of cases are diagnosed among adults age 20–50 years old. Laparoscopic adrenalectomy has become standard treatment for pheochromocytoma of the adrenal gland. The safety and efficacy of laparoscopic approach to resection of extra-adrenal pheochromocytoma in the pediatric population has not been established. DiscussionWe present an interesting case of a 12-year-old female diagnosed with a functional pheochromocytoma of the Organ of Zuckerkandl. Following preoperative optimization of blood pressure, she underwent successful tumor resection via a minimally invasive laparoscopic approach. The operation was completed without intraoperative complication. She was discharged home the following day with resolution of symptoms. She continues to do well in follow up. ConclusionWe demonstrate the successful laparoscopic resection of pheochromocytoma localized to the Organ of Zuckerkandl in a pediatric patient.
ISSN:2213-5766
2213-5766
DOI:10.1016/j.epsc.2021.102165