Epithelioid Hemangioendothelioma of Spleen and Bone: A Case Report

Epithelioid hemangioendothelioma (EHE) is a rare vascular tumor that can originate in various parenchymatous organs, soft tissue, and bone. Extrahepatic involvement is exceedingly rare. In this case, multifocal disease in the spleen and bone was present. Bone lesions showed a target appearance. Sple...

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Bibliographic Details
Published in:Journal of the Belgian Society of Radiology 2024-06, Vol.108 (1), p.64-64
Main Authors: Denolf, Melvin, Rappaport, Annelies, Delvaux, Sigrun
Format: Article
Language:English
Subjects:
camta1
epithelioid hemangioendothelioma
focal splenic lesion
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Summary:Epithelioid hemangioendothelioma (EHE) is a rare vascular tumor that can originate in various parenchymatous organs, soft tissue, and bone. Extrahepatic involvement is exceedingly rare. In this case, multifocal disease in the spleen and bone was present. Bone lesions showed a target appearance. Splenic lesions showed delayed enhancement of solid components with persistent rim enhancement. A bone biopsy with CAMTA1 staining confirmed the diagnosis. The presence of multifocal bone and splenic lesions can raise suspicion of EHE when other multifocal diseases are excluded.
ISSN:2514-8281
2514-8281
DOI:10.5334/jbsr.3600