Novel use of covered stents to treat profound cyanosis in a hepatic vein exclusion Fontan

Fontan completion in patients with complex cardiac anatomy, and specifically heterotaxy syndrome, can present unique physiologic considerations. For example, existing venous connections may be "unmasked" after a cavopulmonary anastomosis operation. We present the case of a child with heter...

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Bibliographic Details
Published in:Annals of pediatric cardiology 2019-01, Vol.12 (1), p.60-63
Main Authors: Batlivala, Sarosh, Ebeid, Makram
Format: Article
Language:English
Subjects:
Anatomy & physiology
Cardiovascular surgery
Case Report
Case studies
Congenital heart disease
covered stents
Cyanosis
Fontan
Health aspects
Intubation
Liver
Patients
Pediatric research
Pediatric surgery
Physiology
Pulmonary arteries
Stents
Veins & arteries
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Description
Summary:Fontan completion in patients with complex cardiac anatomy, and specifically heterotaxy syndrome, can present unique physiologic considerations. For example, existing venous connections may be "unmasked" after a cavopulmonary anastomosis operation. We present the case of a child with heterotaxy, dextrocardia, single-ventricle physiology, and anomalous hepatic venous drainage that resulted in profound shunting and cyanosis. We addressed the problem utilizing a novel strategy with a "fenestrated" covered stent.
ISSN:0974-2069
0974-5149
DOI:10.4103/apc.APC_125_18