Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS

Prader-Willi syndrome (PWS) is the most prevalent syndromic form of obesity, which starts during early childhood in the setting of hyperphagia. Due to the development of obesity, there is a high prevalence of obstructive sleep apnea (OSA) among these patients. This case report presents a patient wit...

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Bibliographic Details
Published in:Case reports in medicine 2023-04, Vol.2023, p.9925144-4
Main Authors: Hwig, Nauras, Diaz-Abad, Montserrat, Peng, Victor T., So, Jennifer Y., Lasso-Pirot, Anayansi
Format: Article
Language:English
Subjects:
Abdomen
Apnea
Blood
Case Report
Children
Drug therapy
Failure
Gas exchange
Hyperphagia
Hypoventilation
Hypoxia
Intervention
Laboratories
Mechanical ventilation
Obesity
Ostomy
Patients
Pediatrics
Prader-Willi syndrome
Respiratory agents
Respiratory failure
Respiratory insufficiency
Severe acute respiratory syndrome coronavirus 2
Sleep
Sleep apnea
Sleep apnea syndromes
Sleep disorders
Tracheotomy
Ventilators
Weight control
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Summary:Prader-Willi syndrome (PWS) is the most prevalent syndromic form of obesity, which starts during early childhood in the setting of hyperphagia. Due to the development of obesity, there is a high prevalence of obstructive sleep apnea (OSA) among these patients. This case report presents a patient with PWS with morbid obesity, severe OSA, and obesity hypoventilation syndrome admitted to the hospital for hypoxemic and hypercapnic respiratory failure. Noninvasive ventilation (NIV) with average volume-assured pressure support, a newer NIV modality, was used successfully to treat this patient, achieving major clinical and gas exchange improvement both during the hospitalization and long term after discharge.
ISSN:1687-9627
1687-9635
DOI:10.1155/2023/9925144