Giant Darier-Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report

Darier-Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an e...

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Bibliographic Details
Published in:Journal of medical case reports 2021-03, Vol.15 (1), p.120-120, Article 120
Main Authors: Triki, A, Aloui, M, Ghalleb, M, Jbir, I, Naceur, Ben, Hassouna, J Ben, Chargui, R, Rahal, K
Format: Article
Language:English
Subjects:
Abdomen
Abdomen - diagnostic imaging
Abdomen - surgery
Cancer
Case Report
Case reports
Darier–Ferrand dermatofibrosarcoma
Dermatofibrosarcoma - surgery
Humans
Male
Metastasis
Middle Aged
Neoplasm Recurrence, Local
Patients
Pelvis
Pelvis - diagnostic imaging
Pelvis - surgery
Plastic surgery
Radiation therapy
Reconstructive surgery
Recurrent
Reproductive organs
Sarcoma
Skin
Skin & tissue grafts
Skin cancer
Skin Neoplasms - surgery
Surgery, Plastic
Surgical resection
Ultrasonic imaging
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Summary:Darier-Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
ISSN:1752-1947
1752-1947
DOI:10.1186/s13256-021-02687-8