Porokeratosis of Mibelli--literature review and a case report

Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with...

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Bibliographic Details
Published in:Anais brasileiros de dermatología 2013-12, Vol.88 (6 Suppl 1), p.179-182
Main Authors: Ferreira, Flávia Regina, Santos, Leopoldo Duailibe Nogueira, Tagliarini, Fernando Augusto Nogueira Mendes, Lira, Marcia Lanzoni de Alvarenga
Format: Article
Language:English
Subjects:
Case Report
Child
Child, Preschool
DERMATOLOGY
Facial Dermatoses - pathology
Female
Humans
Parakeratosis
Porokeratosis
Porokeratosis - pathology
Skin - pathology
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Summary:Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.
ISSN:0365-0596
1806-4841
1806-4841
0365-0596
DOI:10.1590/abd1806-4841.20132721