Single coronary ostium in a patient with quadricuspid aortic valve combined with aneurysmal ascending aortic dilatation

• Published in: Journal of cardiothoracic surgery 2017-07, Vol.12 (1), p.59-59, Article 59
• Main Authors: Kim, Do Yeon, Kim, Hwan Wook
• Format: Article
• Language: English
• Subjects: Abnormalities, Multiple; Aneurysmal ascending aortic dilatation; Aortic Aneurysm, Thoracic - congenital; Aortic Aneurysm, Thoracic - diagnosis; Aortic Aneurysm, Thoracic - surgery; Aortic Valve - abnormalities; Aortic Valve - diagnostic imaging; Aortic Valve - surgery; Aortic Valve Insufficiency - congenital; Aortic Valve Insufficiency - diagnosis; Aortic Valve Insufficiency - surgery; Cardiac Surgical Procedures - methods; Care and treatment; Case Report; Computed Tomography Angiography; Coronary Vessel Anomalies - diagnosis; Coronary Vessel Anomalies - surgery; Coronary Vessels - diagnostic imaging; Coronary Vessels - surgery; Diagnosis, Differential; Echocardiography; Female; Heart valve diseases; Heart Valve Prosthesis; Humans; Imaging, Three-Dimensional; Middle Aged; Multidetector Computed Tomography; Patient outcomes; Quadricuspid aortic valve; Single coronary ostium
• ISSN: 1749-8090; 1749-8090
• DOI: 10.1186/s13019-017-0622-4

The presence of a fourth aortic valve cusp (quadricupsid aortic valve) is a rare congenital malformation and is often accompanied by other anomalies of the adjacent cardiovascular structures. Among these concomitant anomalies, simultaneous association of both a single coronary ostium and aneurysmal ascending aortic dilation in combination with the quadricupsid aortic valve has not been reported yet. We experienced the case of a 56-year-old female patient presenting as aortic regurgitation resulted from malcoaptation of quadricupsid aortic valve. The patient had also accompanying aneurysmal ascending aortic dilatation and coronary ostial anomaly. Surgical correction (aortic valve replacement with mechanical devices and supracoronary aortic replacement with prosthetic graft) was performed without any complications. The technological development of preoperative imaging studies enable the physician to encounter the quadricuspid aortic valve with other associated malformations more often unlike previous reports. With review on the quadricuspid aortic valve, we discussed a surgical considerations for the treatment of this anomaly.