Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome

AbstractCutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an...

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Bibliographic Details
Published in:Annals of hepatology 2015-05, Vol.14 (3), p.416-419
Main Authors: González-Moreno, Emmanuel I, Cámara-Lemarroy, Carlos R, Borjas-Almaguer, David O, Martínez-Cabriales, Sylvia A, Paz-Delgadillo, Jonathan, Gutiérrez-Udave, Rodrigo, Ayala-Cortés, Ana S, Ocampo-Candiani, Jorge, Cortéz-Hernández, Carlos A, Maldonado-Garza, Héctor J
Format: Article
Language:English
Subjects:
Adult
Amyloid
Amyloidosis, Familial - diagnosis
Amyloidosis, Familial - etiology
Amyloidosis, Familial - immunology
Autoimmunity
Biopsy
Cholestasis
Diagnosis, Differential
Gastroenterology and Hepatology
Hepatitis, Autoimmune - complications
Hepatitis, Autoimmune - diagnosis
Hepatitis, Autoimmune - immunology
Humans
Liver - pathology
Liver Cirrhosis, Biliary - complications
Liver Cirrhosis, Biliary - diagnosis
Liver Cirrhosis, Biliary - immunology
Male
Pruritus
Skin - pathology
Skin Diseases, Genetic - diagnosis
Skin Diseases, Genetic - etiology
Skin Diseases, Genetic - immunology
Syndrome
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Description
Summary:AbstractCutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.
ISSN:1665-2681
DOI:10.1016/S1665-2681(19)31283-9