Extrahepatic hepatoblastoma- an extremely rare occurrence

6 year old presented with hard non tender mass in epigastric region. On radiological examination a well defined mass was seen in the lesser sac without the liver involvement. On histopathological evaluation by trucut biopsy, diagnosis of extrahepatic hepatoblastoma was made. The boy underwent 4 cycl...

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Bibliographic Details
Published in:Journal of pediatric surgery case reports 2021-04, Vol.67, p.101815, Article 101815
Main Authors: Sarin, Y.K., Narang, R., Tomar, R., Kumar, S., Giri, P., Radhakrishnan, A.
Format: Article
Language:English
Subjects:
Extrahepatic hepatoblastoma
Hepatoblastoma
Tumor excision
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Summary:6 year old presented with hard non tender mass in epigastric region. On radiological examination a well defined mass was seen in the lesser sac without the liver involvement. On histopathological evaluation by trucut biopsy, diagnosis of extrahepatic hepatoblastoma was made. The boy underwent 4 cycles of neoadjuvant chemotherapy which caused the tumor to shrink by 40%. The patient underwent resection of tumor without any complications. The post-operative histopathology also revealed Hepatoblastoma (Fetal type). The patient underwent post operative chemotherapy and has an event free survival of 6 months till now. We present this case, as to the best of our knowledge; this is a rare case of isolated hepatoblastoma arising from extrahepatic tissue.
ISSN:2213-5766
2213-5766
DOI:10.1016/j.epsc.2021.101815