Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome

Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of mol...

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Bibliographic Details
Published in:Frontiers in pediatrics 2022-06, Vol.10
Main Authors: Chan, Yat Chi, Kan, Amanda N. C., Yuen, Liz Y. P., Wan, Innes Y. P., Fung, Kevin K. F., Cheung, Yiu-fai, Leung, Karen K. Y., Ku, Dennis T. L., Liu, Anthony P. Y.
Format: Article
Language:English
Subjects:
low-grade fibromyxoid sarcoma
mediastinal syndrome
Pediatrics
RNA-sequencing
thoracic tumor
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Summary:Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of molecular profiling and review reported cases of pediatric thoracic LGFMSs.
ISSN:2296-2360
2296-2360
DOI:10.3389/fped.2022.885068