A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma

Epithelioid angiomyolipoma (EAML) is a subtype of angiomyolipoma, the most common benign renal tumour and usually asymptomatic until adulthood. This paper reports a patient with EAML identified at 30 months, the youngest age of presentation with this tumour reported in the literature. In this case t...

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Bibliographic Details
Published in:Urology case reports 2020-01, Vol.28, p.101035, Article 101035
Main Authors: Kakaje, Ameer, Mujahed, Raghad, Hamdan, Othman, Hakim, Jihad
Format: Article
Language:English
Subjects:
Idiopathic chylothorax
Octreotide
Paediatric epithelioid angiomyolipoma
Pediatrics
Tuberous sclerosis
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Summary:Epithelioid angiomyolipoma (EAML) is a subtype of angiomyolipoma, the most common benign renal tumour and usually asymptomatic until adulthood. This paper reports a patient with EAML identified at 30 months, the youngest age of presentation with this tumour reported in the literature. In this case the tumour was extremely large andwas successfully surgically removed. Furthermore, the patient had no other TS features, presented with acute symptoms, and had bilateral idiopathic chylothorax which was managed by octreotide and diet.
ISSN:2214-4420
2214-4420
DOI:10.1016/j.eucr.2019.101035