Retroperitoneal low‐grade fibromyxoid sarcoma

Introduction Low‐grade fibromyxoid sarcoma is an uncommon deep‐seated soft‐tissue sarcoma that occurs rarely in young adults and children. Although surgical resection provides a long‐term prognosis, late local recurrence and metastasis may occur. Case presentation A 44‐year‐old woman with no prior m...

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Bibliographic Details
Published in:IJU case reports 2024-05, Vol.7 (3), p.255-258
Main Authors: Noguchi, Takeaki, Suzuki, Takahisa, Shibata, Yosuke, Koizumi, Mitsuyuki, Osaka, Kimito, Kishida, Takeshi
Format: Article
Language:English
Subjects:
Abdomen
Antigens
Case Report
Case Reports
Chemotherapy
Diaphragm (Anatomy)
Evans tumor
low‐grade fibromyxoid sarcoma
Medical imaging
Medical prognosis
Metastasis
Patients
Prostheses
Radiation therapy
retroperitoneal sarcoma
Sarcoma
Surgery
Sutures
Tumors
Young adults
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Summary:Introduction Low‐grade fibromyxoid sarcoma is an uncommon deep‐seated soft‐tissue sarcoma that occurs rarely in young adults and children. Although surgical resection provides a long‐term prognosis, late local recurrence and metastasis may occur. Case presentation A 44‐year‐old woman with no prior medical history presented with breathing and abdominal discomfort. Contrast‐enhanced computed tomography scan revealed a retroperitoneal tumor protruding into the thoracic cavity and pleural effusion on the left side. Tumor biopsy revealed sarcoma. We performed complete resection of the tumor along with part of the diaphragm and replaced the diaphragm with a prosthetic patch. Histopathologic findings indicated low‐grade fibromyxoid sarcoma. The patient experienced no postoperative complications and received no adjuvant therapy. Furthermore, she survived 4 years after surgery without recurrence. Conclusion Complete surgical resection is effective for low‐grade fibromyxoid sarcoma; therefore, it is important to plan appropriately for complete resection when biopsy reveals malignant findings.
ISSN:2577-171X
2577-171X
DOI:10.1002/iju5.12718