Perianal alveolar soft-part sarcoma: a rare case

Background Alveolar soft part sarcoma (ASPS) is a rare diagnosis in the perianal region. Methods we describe the clinical presentation, pathological findings and differential diagnosis of a rare case of perianal ASPS. We also describe the importance of the preoperative embolization of the hypervascu...

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Bibliographic Details
Published in:Central European journal of medicine 2014-04, Vol.9 (2), p.246-249
Main Authors: Alonso-Gómez, Jaime, Caro-Cuenca, María Teresa, Membrives-Obrero, Antonio, Ortega-Salas, Rosa, Gallardo-Valverde, José María, Orti-Rodríguez, Rafael, Peña, Sebastián Rufián
Format: Article
Language:English
Subjects:
Alveolar sarcoma
Biomedicine
Case Report
Internal Medicine
Maternal and Child Health
Medicine
Medicine & Public Health
Molecular
Perianal
Reproductive Medicine
Surgery
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Summary:Background Alveolar soft part sarcoma (ASPS) is a rare diagnosis in the perianal region. Methods we describe the clinical presentation, pathological findings and differential diagnosis of a rare case of perianal ASPS. We also describe the importance of the preoperative embolization of the hypervascularised masses to prevent surgical bleeding. Conclusions clinical and pathological findings are essential for the diagnosis, specifically by immunochemistry and molecular techniques, as the demonstration of ASPL/TFE3 fusion transcript became indispensable in some cases. Preoperative embolization of the hypervascularised masses may prevent uncontrollable surgical bleeding.
ISSN:1895-1058
2391-5463
1644-3640
2391-5463
DOI:10.2478/s11536-012-0145-2