Anomalous origin of the right coronary artery from the pulmonary artery associated with an aortopulmonary window

Anomalous origin of the right coronary artery (RCA) from the pulmonary artery is a rare entity that causes chronic left-to-right shunting of blood from the RCA, through the coronary collaterals into the pulmonary artery. This results in persistent myocardial ischemia and ventricular dysfunction. Ass...

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Bibliographic Details
Published in:Annals of pediatric cardiology 2018-09, Vol.11 (3), p.325-327
Main Authors: Bhat, Padebettu, Chandrashekar, Chandana, Mallikarjun, Divya, Girish Gowda, S
Format: Article
Language:English
Subjects:
Abnormalities
Anomalous origin of the right coronary artery from the pulmonary artery
aortopulmonary window
Atrial septal defects
Care and treatment
Case studies
Coronary arteries
Coronary vessels
Defects
Electrocardiography
intrapulmonary baffle
Ischemia
Pediatric cardiology
Pulmonary arteries
Pulmonary artery
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Summary:Anomalous origin of the right coronary artery (RCA) from the pulmonary artery is a rare entity that causes chronic left-to-right shunting of blood from the RCA, through the coronary collaterals into the pulmonary artery. This results in persistent myocardial ischemia and ventricular dysfunction. Association of this anomaly with an aortopulmonary window worsens the condition further due to an additional shunt. We encountered a combination of these two anomalies along with an ostium secundum atrial septal defect in a 10-month-old baby who presented with excessive crying and failure to thrive. Evaluation by transthoracic echocardiography and cardiac computed tomography scan confirmed the diagnosis. Intrapulmonary baffle was done using a pericardial patch to connect the RCA origin to ascending aorta through the aortopulmonary window, similar to Takeuchi procedure. Concomitantly, ostium secundum atrial septal defect was also closed.
ISSN:0974-2069
0974-5149
DOI:10.4103/apc.APC_65_18