Schwartz-Matsuo syndrome: An important cause of secondary glaucoma

We report a case of Schwartz-Matsuo syndrome that highlights the pathophysiology, diagnostic challenges, and management considerations of this rare disease. 31-year-old man with a history of left eye cataract presented with left eye photophobia and elevated intraocular pressure (IOP) of 64 mm Hg. Vi...

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Bibliographic Details
Published in:American journal of ophthalmology case reports 2020-03, Vol.17, p.100586, Article 100586
Main Authors: Etheridge, Tyler, Larson, Jennifer C., Nork, T. Michael, Momont, Anna C.
Format: Article
Language:English
Subjects:
Case Report
Open-angle glaucoma
Retinal detachment
Schwartz-Matsuo syndrome
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Summary:We report a case of Schwartz-Matsuo syndrome that highlights the pathophysiology, diagnostic challenges, and management considerations of this rare disease. 31-year-old man with a history of left eye cataract presented with left eye photophobia and elevated intraocular pressure (IOP) of 64 mm Hg. Visual acuity 20/40. Open angles with an increased pigment of trabecular meshwork by gonioscopy, 2 + anterior chamber (AC) cell, superior retinal detachment, and 0.6 cup-to-disc ratio. Electron microscopy of AC fluid demonstrated outer segments of photoreceptors. IOP was lowered with oral and topical ophthalmic antihypertensives. Retinal detachment was treated with pars plana vitrectomy with endolaser, gas tamponade, and AC paracentesis. Follow-up VA 20/20 with normal IOP. Schwartz-Matsuo syndrome is characterized by elevated IOP with marked fluctuations, open angles, aqueous cells, and retinal detachment. Diagnosis is supported by electron microscopy of AC fluid with outer segments of photoreceptors. Treatment includes retinal detachment repair and antihypertensive therapy.
ISSN:2451-9936
2451-9936
DOI:10.1016/j.ajoc.2020.100586