Renal Angiomyolipoma Mimicking a Well-Differentiated Retroperitoneal Liposarcoma

A 37-year-old Burmese woman presented with an incidentally found retroperitoneal fat-containing tumor. The tumor was 9 cm in the longest diameter, surrounding the right kidney, and composed of homogenous adipose tissue with thickened septum-like structures and spotty nonadipose structures, which wer...

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Bibliographic Details
Published in:Case reports in urology 2020-09, Vol.2020 (2020), p.1-5
Main Authors: Koga, Fumitaka, Okuma, Tomotake, Motoi, Toru, Ikuta, Shuzo, Takemura, Kosuke, Ito, Masaya, Fuse, Honoka, Kataoka, Madoka
Format: Article
Language:English
Subjects:
Abdomen
Adipose tissues
Aneurysms
Biopsy
Calcification
Case Report
Case reports
CT imaging
Embolization
Gastric cancer
Hemorrhage
Kidneys
Liposarcoma
Magnetic resonance imaging
Sarcoma
Smooth muscle
Surgery
Surveillance
Tumors
Urology
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Summary:A 37-year-old Burmese woman presented with an incidentally found retroperitoneal fat-containing tumor. The tumor was 9 cm in the longest diameter, surrounding the right kidney, and composed of homogenous adipose tissue with thickened septum-like structures and spotty nonadipose structures, which were enhanced on contrast-enhanced computed tomography and magnetic resonance imaging. The tumor did not show either a beak sign or synchronous angiomyolipoma-like lesion in the kidneys. The tumor had irregular septa, thin blood vessels, and spotty small soft-tissue nodules. The tumor did not contain any heterogeneously enhanced solid lesions suspicious for dedifferentiated liposarcomas. Based on these imaging findings, a clinical diagnosis of a well-differentiated liposarcoma was made. Under the consensus of a multidisciplinary cancer board, she was recommended to undergo core-needle biopsy to confirm the clinical diagnosis. However, she declined to undergo biopsy for financial reasons. She underwent kidney-sparing retroperitoneal tumor resection. Histopathologically, the tumor was an angiomyolipoma with positive immunostaining for HMB45 and Melan A. The present case suggests the importance of core-needle biopsy prior to surgical intervention for retroperitoneal fat-containing tumors.
ISSN:2090-696X
2090-6978
DOI:10.1155/2020/8812057